The progressive supranuclear palsy psp or steelerichardsonolzsewski syndrome is a rapidly progressing degenerative disease of unknown origin brusa et al. Cases how to cite bluebook quick reference akron law. Cases bluebook legal citation tarlton law library at tarlton law. Generations of law students, lawyers, scholars, judges, and other legal professionals have relied on the bluebooks unique system of citation in their writing. Characterized by paralysis of eye movements, difficulty talking and swallowing, body trunk rigidity, gait ataxia, and dementia, the disease progresses rapidly over a 68 year time span. Communication impairments in people with progressive. A case of atypical progressive supranuclear palsy italian. In addition to parkinsonism, the clinical symptoms include early postural instability, supranuclear gaze palsy, and cognitive decline. We are proud to bring you the 2020 curepsp guidebook. The bluebook style guide is used in the american legal profession for citation of all relevant sources.
After studying the material presented here, you will be able to. Progressive supranuclear palsy genetic and rare diseases. Studies have demonstrated that psp can present clinically as an atypical dementing syndrome dominated by a progressive apraxia of speech aos and aphasia. Together with john steele and jerzy olszewski 2, they reported extensive subcortical neurofibrillary degeneration predominantly in the globus pallidus, subthalamic nucleus, substantia nigra, and dentate nucleus. Progressive supranuclear palsy is a rare neurological condition affecting parts of the brain that control walking, eye movements, balance, speech and swallowing. Progressive supranuclear palsy psp is a rare progressive condition that can cause problems with balance, movement, vision, speech and swallowing.
The loss of nerve cells causes palsy, or paralysis, that slowly gets worse as. Characteristic features of psp and its variants include vertical supranuclear gaze palsy, postural instability with unexplained falls, akinesia, and cognitive dysfunction. The goal of this continuing education program about progressive supranuclear palsy is to provide physical therapists with tools to identify clinical symptoms, evidencebased physical therapy, and additional resources for the family and healthcare team. The causes of psp are unknown, although current research suggests that it is caused by a combination of environmental and genetic factors. The condition leads to symptoms including loss of balance, slowing of movement, difficulty moving the eyes, and dementia. The registry is an online database to collect information from those affected by all types psp, cbd, and related diseases. Welcome to curepsp neurodegeneration support assistance.
Males and females are affected the same equally and there is no racial, geographical or occupational predilection. The official patients sourcebook on progressive supranuclear palsy. Pathologic diagnosis was confirmed by internationally agreed criteria. Approximately 6 people per 100,000 population have psp. Progressive supranuclear palsy is a degenerative disease involving the gradual deterioration and death of specific volumes of the brain. Psp is a very individual condition and every case is unique. Citing court cases bluebook legal citations research guides at. This leads to serious and permanent problems with balance and the way you walk. The symptoms typically become more severe over several years, although the speed at which. Progressive supranuclear palsy pathology caused by a. Symptoms usually begin between the ages of 60 and 70.
Georgetown law library provides a great overview of the bluebook and the basic concepts of legal citation for cases, statutes, and other. The risk factors of progressive supranuclear palsy psp, a rare but severe parkinsonian syndrome, are poorly known. Bluebook citation for legal materials purdue writing lab. Although some case reports of a similar combination of the clinical. Progressive supranuclear palsy risks, symptoms and leading. Reporters include all court opinions in chronological order. The official patients sourcebook on progressive supranuclear. There is no known cure for psp and management is primarily supportive. Progressive supranuclear palsy psp is the second most frequent cause of degenerative parkinsonism. Characteristic features of psp and its variants include vertical supranuclear gaze palsy, postural instability with. Progressive supranuclear palsy simple english wikipedia.
Nontechnical summary if youre having trouble reading this, try enlarging the type. Feb 07, 2020 progressive supranuclear palsy is an uncommon brain disorder that causes serious problems with walking, balance and eye movements, and later with swallowing. Bluebook rule 10 covers how cases should be cited in legal documents. Progressive supranuclear palsy progressive supranuclear palsy psp.
He was exposed to agent orange many times during his service years 19501971. The disorder results from deterioration of cells in areas of your brain that control body movement, coordination, thinking and other important functions. In this case, combination of clinical presentation with atypical parkinsonism, eye movement abnormalities and characteristic mri features make the diagnosis of progressive supranuclear palsy psp highly likely. Adam murphy, a reporter for cbs46 learned of his mothers diagnosis of progressive supranuclear palsy, psp, in 2010 and decided to use his reporter platform to help her, originally reported continue reading reporter fundraises for progressive supranuclear palsy research. Progressive supranuclear palsy disease reference guide. It is not contagious, does not run in families and can affect men and women from all nationalities and lifestyles. It was very heartbreaking for my mother and i watching him go from being a very active man to becoming a shell of the. Progressive supranuclear palsy psp is a rare and progressive condition in which increasing numbers of brain cells become damaged over time.
Many neurodegenerative diseases are difficult to establish with certainty. A revised and updated directory for the internet age icon health publications on. This signature publication features 150 pages of the latest information on psp, cbd, and msa and is the perfect reference for patients, family, carepartners, and health professionals. My father jim wofford, served in the army for over 20 years. The condition leads to symptoms including loss of balance, slowing of movement, difficulty moving the eyes, dementia. Problems, cases, and materials 2006 when you are citing to a work that has been published by the same publisher more than once, you should cite the edition and the year it was published in. Category of impairments, neurological disorders 11. Although it has recently been linked to environmental factors there is no evidence that exposure to any specific chemical causes psp. In this case, combination of clinical presentation with atypical parkinsonism, eye movement abnormalities and characteristic mri features make the diagnosis of progressive supranuclear palsy psp. Progressive supranuclear palsy psp is an uncommon, but debilitating, neurological disease. Josephs ka, dickson dw 2003 diagnostic accuracy of progressive supranuclear palsy in the society for progressive supranuclear palsy brain bank.
Progressive supranuclear palsy symptoms and causes mayo. As a member of the registry, you can help us advance the science and move faster toward finding treatments and cures. Neurodegenerative disease chapter 9 atlas of gross. The category is also for use in multiple coding to identify these conditions resulting from any cause. For language access assistance, contact the ncats public information officer. Case citations always use the case name parties, volume, reporter, page, and year. Progressive supranuclear palsy psp is a neurodegenerative extrapyramidal syndrome. You may fall a lot or find that you feel a bit rigid or uncomfortable when you walk. The causes of psp are unknown, although current research suggests that it is caused. Progressive supranuclear palsy is a rare brain disease affecting only a few thousand people in the u. Psp cases are often split into two subgroups, psprichardson, the classic type, and pspparkinsonism, where a shortterm response to levodopa can be obtained.
Progressive supranuclear palsy psp is a neurological condition caused by the premature loss of nerve cells in certain parts of the brain. Clifford richardson 1 described an unusual syndrome of supranuclear gaze palsy, and progressive axial rigidity, pseudobulbar palsy, and mild dementia. Legal citation legal studies everett library at everett library. People with progressive supranuclear palsy psp develop a range of difficulties with balance, movement, vision, speech and swallowing. Its caused by increasing numbers of brain cells becoming damaged over time. Progressive supranuclear palsy definition of progressive. Progressive supranuclear palsy is an uncommon brain disorder that causes serious problems with walking, balance and eye movements, and later with swallowing. Persons diagnosed, currentformer caregivers, family, and friends can join. Psp patients display impairments in executive functioning, memory, and other cognitive abilities gerstenecker et al. Keep in mind, that progressive supranuclear palsy psp is an idiopathic neurodegnerative disease with parkinsonslike symptoms.
Nov 19, 2009 progressive supranuclear palsy psp is an uncommon neurodegenerative disorder often misdiagnosed, most frequently as parkinsons disease pd. Psp may be mistaken for other neurodegenerative diseases such as parkinsons and alzheimers. Progressive supranuclear palsy symptoms and causes. He was diagnosed with progressive supranuclear palsy in 1990 and passed away in 1996. More recently, a clinical genetic study of familial psp suggested that hereditary. Progressive supranuclear palsy psp symptoms stanford. Mar 16, 2016 keep in mind, that progressive supranuclear palsy psp is an idiopathic neurodegnerative disease with parkinsonslike symptoms. Progressive supranuclear palsy psp posted in personal perspective problems with unsteadiness, visual disturbances and behavioural changes can be symptomatic of a myriad of conditions, but they are also key signs of the neurological condition progressive supranuclear palsy psp as one gp discovered. Then over time they become more noticeable and severe.
The guide takes account of the latest editions of the alwd guide to legal citation 2017, the bluebook, published in 2015, and the supreme courts style. Genetic influences are increasingly being implicated in the aetiology of psp. Progressive supranuclear palsy definition progressive supranuclear palsy psp. Progressive supranuclear palsy risks, symptoms and. Often, the first sign is a problem with balance while walking. Progressive supranuclear palsy psp, also known as steele richardson olszewski syndrome, is an uncommon but not rare parkinsonian syndrome. Much has been learnt about this sporadic illness of middle and late life although its cause remains unknown, and its treatment continues to be difficult. Oct 17, 2018 progressive supranuclear palsy psp, also known as steelerichardsonolszewski syndrome, is a neurodegenerative disease that affects cognition, eye movements, and posture. It was very heartbreaking for my mother and i watching him go from being a very active man to becoming a shell of the man he. Five decades ago, steele, richardson, and olszewski 1964 described an unusual clinical and neuropathological profile of nine patients with a progressive neurological condition displaying supranuclear gaze palsy, axial rigidity, dysarthria, pseudobulbar and mental signs with mild subcortical dementia. Dyskinesia is an occasional but rare complication of treatment. Progressive supranuclear palsy archives patient worthy. The condition tends to develop gradually, which means it can be mistaken for another, more common, condition at first.
Legalease launched a legal citation generator that enables its users to create citations in the bluebook format. Progressive supranuclear palsy psp is a degenerative disease involving the gradual deterioration and death of specific volumes of the brain. New and reliable mri diagnosis for progressive supranuclear palsy. Symptoms of progressive supranuclear palsy psp tend to start out subtly.
The loss of nerve cells causes palsy, or paralysis, that slowly gets worse as the disease progresses. Part i explores basic techniques to researching progressive supranuclear palsy e. Psp may be mistaken for other neurodegenerative diseases such as alzheimers. Curepsp is the leading nonprofit organization working to increase awareness, advocate for patients and families, and fund research for devastating prime of life neurodegenerative diseases, including progressive supranuclear palsy psp, corticobasal degeneration cbd, and multiple system atrophy msa. Progressive supranuclear palsy psp or steelerichardsonolszewski syndrome is a neurodegenerative disease of middle and late age. We use cookies to distinguish you from other users and to provide you with a better experience on our websites. Symptoms are very different in each person, but may include personality changes, speech.
Books, reports, treatises bluebook legal citation tarlton law. Progressive supranuclear palsy is one of the commonest alternative diagnoses. Identify four symptoms of progressive supranuclear palsy that differentiate. In a diverse and rapidly changing legal profession, the bluebook continues to provide a systematic method by which members of the profession communicate important information to one another about the sources and legal authorities upon. The spectrum of the clinical phenotypes in these families was variable, including 34 typical cases of psp 12 probands plus 22 secondary cases, 3 patients with postural tremor, 3 with dementia, 1 with. It is underdiagnosed not only by general physicians but also by. If you have problems viewing pdf files, download the latest version of adobe reader. To study the risk factors of psp in a case control study among french patients. Author names should be included in full just as they appear in. Additionally, the chicago manual of style recommends its use for all citation of legal material. Progressive supranuclear palsy psp is a rare neurodegenerative disorder in which, classically, patients present with postural instability and falls, parkinsonism, and slowing of vertical saccades litvan et al. Signals are important because they indicate how a cited authority relates to the text.
It affects brain cells that control the movement of your eyes. Introductory signals appear at the beginning of citation sentences. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. This category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. Progressive supranuclear palsy psp is a rare brain disease. Intro for patients and caregivers psp blog and registry.
709 1287 1485 263 289 1000 254 183 862 505 682 1480 1342 1404 787 81 665 471 1310 1121 193 802 833 1237 658 685 963 1098 547 673 1108 758 262 1461 1202 1118 1091 1334 30 228 120 1293